Carcinoid tumour of ampulla of Vater associated with viscero-cutaneous neurofibromatosis.
نویسندگان
چکیده
A case of carcinoid tumour of the ampulla of Vater with viscero-cutaneous neurofibromatosis is reported together with a review of the literature.
منابع مشابه
Primary adenocarcinoma of the duodenum associated with cutaneous neurofibromatosis (von Recklinghausen's disease).
Introduction The association of neurofibromatosis with malignant tumours of the neural crest is well documented. Neurofibromatosis may also be associated with other malignant tumours such as carcinoid of the ampulla of Vater (Barber, 1976), adenocarcinoma of the pancreas (Kellar and Logan, 1977), adenocarcinoma of the colon (Jenkins and Gill, 1972), Wilms' tumour (Stay and Vauter, 1977), rhabdo...
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Patients with neurofibromatosis type 1 are at increased risk of developing carcinoid tumours of the duodenum, particularly in the ampulla of Vater. Aggressive surgery with pancreatoduodenectomy is recommended for all ampullary carcinoid tumours because of their propensity to metastasise. We report a case of a 43-year-old woman with neurofibromatosis type 1, who presented with recurrent epigastr...
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estimated incidence at all anatomic sites of 1 in 12 000. Although 67% of these lesions are found within the gastrointestinal tract, fewer than 1% are located at or near the ampulla of Vater. These periampullary tumours have characteristics that set them apart from carcinoids at other sites, including strong immunohistochemical positivity for somatostatin and presence of psammoma bodies. Althou...
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BACKGROUND Type 1 neurofibromatosis (NF-1) is an autosomal dominant disorder with variable penetrance; approximately 50% of cases present as new mutations CASE REPORT We report a case of a 56 year-old man with Von Recklinghausen's disease, carcinoma of the ampulla of Vater and incidental benign gastrointestinal stromal tumours of the jejunum. CONCLUSIONS Coexistence between ampullary carcin...
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Carcinoid tumours of the common bile duct represent an extremely rare entity. Similarly, primary follicular lymphomas of the ampulla of Vater constitute an infrequent neoplasia. Herein, we report the first case of a synchronous development of a carcinoid tumour of the common bile duct and an ampullary follicular lymphoma that was treated surgically with a Whipple's procedure, due to inability t...
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ورودعنوان ژورنال:
- Postgraduate medical journal
دوره 59 697 شماره
صفحات -
تاریخ انتشار 1983